overview
Bladder exstrophy and surgical repair in a female infant
Bladder exstrophy and surgical repair in a male infant
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Bladder exstrophy (EK straw fee) is a rare birth defect in which the bladder grows outside the fetus. The exposed bladder cannot hold urine or function normally, causing urine to leak (incontinence).Bladder exstrophy Treatment Hyderabad
- The problems caused by bladder exstrophy vary in severity. They can include defects of the bladder, genitals, and pelvic bones, as well as defects of the bowel and reproductive organs.
- Bladder exstrophy can be detected during a routine ultrasound during pregnancy. However, sometimes the defect is not visible until the baby is born. Babies born with bladder exstrophy will need surgery to correct the defects.
symptom
Bladder exstrophy is most common in the larger group of birth defects called the bladder exstrophy-epispadial complex (BEEC). If your child has BEEC, they will have one of the following options:
- Epispadias. It is the less severe form of BEEC in which the tube used to expel urine (urethra) does not fully develop.
Bladder exstrophy. This defect causes the blister to form outside of the body. The bladder is also turned upside down. Usually, bladder exstrophy affects the organs of the urinary tract and the digestive and reproductive systems. There may be defects in the abdominal wall, bladder, genitals, pelvic bones, the last section of the large intestine (rectum), and the opening at the end of the rectum (anus). - Children with bladder exstrophy also have vesicoureteric reflux. This condition causes urine to flow in the wrong direction – from the bladder to the tubes that connect to the kidneys (ureters). Children with bladder exstrophy also have epispadias.
- Cloacal exstrophy. Cloacal exstrophy (kloe-A-kul EK-straw-fee) is the most severe form of BEEC. In this condition, the rectum, bladder, and genitals do not separate completely as the fetus develops. These organs may not be properly formed, and the pelvic bones may also be affected.Bladder exstrophy Treatment Hyderabad
The reasons
Doctors aren’t sure why bladder exstrophy develops. Researchers believe a combination of genetic and environmental factors likely play a role.
- It is known that as the fetus grows, a structure called the cloaca (klo-A-kuh), where the reproductive, urinary, and digestive openings meet, does not develop properly in babies who develop bladder exstrophy. Defects in the cloaca can vary widely depending on the age of the fetus when the developmental defect occurs.
Risk factors
Factors that increase your risk of bladder exstrophy include:
- Family history. Firstborn babies, children of a parent with bladder exstrophy, or siblings of a child with bladder exstrophy are at increased risk of being born with the disease.
- Run. Bladder exstrophy is more common in whites than in other breeds.
- Sex. More boys than girls are born with bladder exstrophy.
- Use of assisted reproduction. Children born with assisted reproductive technology such as IVF are at greater risk of bladder exstrophy.Bladder exstrophy Treatment Hyderabad